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Mother of son with Baclofen Pump
warns others: proceed with caution

 

By Loma Cohn

My son, Michael, who has NBIA, was encouraged by his neurologist to be tested for a Baclofen  Pump implant to help alleviate some of his symptoms.

 

We were given quite a bit of information about the pump and Mike was told very clearly that it would involve a major commitment on his part. But he's an adult, and it was his decision. I still had doubts from the first time we explored this avenue, but supported his right to choose.

 

We were encouraged by the fact that the pump program had grown and matured

considerably. Mike chose the implant. So, on Sept. 11, 2001, while Mike was in surgery, I sat with several family members in the waiting room. The television was on and we watched with horror as the  tragedy unfolded in New York.

 

Mike's recovery was very easy. The results were initially astounding! His speech improved dramatically. His walking steadied to the point that he was able to give up his walker and use a cane. However, these improvements began to diminish after about two months. We have recently learned that this frequently happens when the primary problem is spasticity. The pump apparently is more effective when treating the problem of rigidity.

 

So often we are told what to anticipate, but it's phrased in such bland, non-specific terms that we think, "Okay, we can do this."  For example, when the doctor says,  "You will have to monitor your child,"  we think, "Well, we do that every day, right?"  Wrong.

 

Monitoring in this case means when you notice more rigidity, you must head back to the clinic for an adjustment. When the person is getting too little Baclofen, it's back to the clinic for an adjustment. There's no more just cutting back or increasing the number of pills. Yet, no one told us that Mike might have to go in for adjustments as many as two or three times a week.

 

A few months after the pump was implanted, the catheter separated from the pump. He had gone to the clinic several times because of swelling in that area and was told repeatedly that it was just a fluid buildup. It wasn't. It was the baclofen leaking. Mike had to have surgery to have it fixed.

 

The monitoring warning we didn't get was the most important one of all: When the pump is refilled or adjusted, you receive a computer printout of the dose, frequency, refill date, etc.  Mike always brought them home and filed them. It never occurred to me to read them and because of Mike's vision, he wasn't able to read them.

 

On July 24, 2003, Mike had his pump refilled.  Fortunately, he came home immediately after that. Within thirty minutes of his arrival, he was unconscious. Within three minutes of dialing 911, the police arrived, and the paramedics a few minutes later. Mike went into cardiac and pulmonary arrest.

 

The ambulance rushed him to a trauma center, which fortunately has a pump program. The doctors turned off the pump, as it appeared Mike was overdosing on Baclofen. We learned there is an antidote for an overdose. We faced two choices of treatment:  1) let the Baclofen work its way out of his system, or 2) administer the antidote knowing there was a significant risk of a heart attack. We chose the first option.

 

The physician who had set the pump that morning had made a huge error. It was supposed to be set to deliver a dose every six hours and was actually set to deliver a dose every six minutes.  Mike remained unconscious for about 24 hours and was on a respirator. He seems to have made a good recovery and the only long-term damage we are aware of is some short-term memory loss.

 

Now when he goes for an adjustment, he insists the physician or nurse review the computer printout with him before he leaves.

 

Still, Mike has decided to have the pump removed.  We have learned that it will take about a year before that can be done.

 

I understand that the pump has been effective for some people.  However, I would encourage anyone considering the implant to explore alternatives before making the decision.